Unicornuate Uterus

What is a unicornuate uterus?

To understand unicornuate uterus, a congenital abnormality of the uterus, it's helpful to understand how the uterus is formed. During typical fetal development, two tubelike structures, called the Mullerian ducts, fuse together to create the uterus. The upper portions form the fallopian tubes. If one of the ducts fails to develop, it may result in a single-horned uterus, called a unicornuate uterus. Usually this disorder isn't detected until later in life.

It's estimated that about one in 4,020 women in the general population have unicornuate uterus. Women with a unicornuate uterus sometimes also have a second smaller remnant of a uterus, called a hemi-uterus. This hemi-uterus may or may not be connected to the rest of the uterus. If it's unattached, menstrual blood won't be able to flow out, causing pain. If a hemi-uterus is present, it needs to be removed.

A unicornuate uterus may be able to support a pregnancy, but a cesarean section may be required. There is also an increased risk of preterm labor and miscarriage because of the small size of the uterus.

How we care for unicornuate uterus

At the Boston Children's Hospital Division of Gynecology and the Center for Congenital Anomalies of the Reproductive Tract, an interdisciplinary team of pediatricians, gynecologists, urogynecologists and colorectal surgeons will work to find the best treatment for your daughter's unicornuate uterus.