Pulmonary Vein Stenosis | Symptoms & Causes

What are the symptoms of pulmonary vein stenosis?

Symptoms of pulmonary vein stenosis can emerge very suddenly—especially in infants—or it can also progress gradually over time. The warning signs in both cases may include:

  • shortness of breath
  • rapid heartbeat
  • rapid, shallow breathing
  • fatigue
  • poor appetite
  • pale or “washed-out” skin hue
  • blue-tinged appearance, called cyanosis, of the skin, lips or nail beds

You should seek treatment from a qualified medical professional right away if you notice any of these symptoms in your child.

What causes pulmonary vein stenosis?

The exact cause of pulmonary vein stenosis is still unknown.

Sometimes, it can occur as a complication of another heart or lung problem, such as complex congenital heart disease or chronic lung disease.

The intraluminal form of pulmonary vein stenosis may be linked to an overgrowth of connective tissue cells. These are the cells that are normally responsible for closing and healing wounds within the body.