Choroid Plexus Brain Tumor

What is a choroid plexus brain tumor?

Choroid plexus brain tumors develop in the tissue located in the spaces of the brain called ventricles. This tissue makes cerebrospinal fluid (CSF), which surrounds the brain and spinal cord. These rare tumors are seen more often in younger children. Between 10 and 20 percent of brain tumors that occur within the first year of life are choroid plexus tumors.

How are choroid plexus tumors classified?

Successfully treating your child’s brain tumor depends on what type of choroid plexus tumor your child has. Doctors at Dana-Farber/Boston Children's will classify your child's tumor as one of the following types:

  • Choroid plexus papillomas (CPPs): These are one of two types of choroid plexus tumor that grow slowly, rarely spread and are by far more common.
  • Atypical plexus papillomas (APPs): Like CPPs, these tumors grow more slowly than their aggressive counterparts and rarely spread.
  • Choroid plexus carcinomas (CPCs) grow more aggressively and are more likely to spread than either APPs or CPPs. CPCs are less common, accounting for 25-35 percent of all choroid plexus tumors.

Choroid plexus papillomas are often easier to treat than carcinomas. An APP can act more aggressive but usually behaves like a CPP.

How we care for choroid plexus brain tumors

Children with choroid plexus tumors are treated through the Brain Tumor Center at Dana-Farber/Boston Children's Cancer and Blood Disorders Center, a world-renowned destination for children with malignant and non-malignant brain and spinal cord tumors. Our brain tumor specialists have extensive expertise in treating all types of neural tumors, including choroid plexus tumors.