Related Conditions and Treatments
Complex Biventricular Repair
Complex biventricular repair is an option for children with single ventricle heart defects to achieve two-ventricle circulation.
Double Outlet Right Ventricle (DORV)
Double outlet right ventricle (DORV) is a type of rare congenital heart condition.
Ebstein’s anomaly is a rare heart defect that affects the tricuspid valve.
Heterotaxy is a rare condition where many organs in the body can be formed abnormally, in the wrong position, or even missing.
Hypoplastic Left Heart Syndrome (HLHS)
Hypoplastic left heart syndrome is a spectrum of heart diseases in which the left-heart structures are underdeveloped.
Pulmonary atresia occurs when the pulmonary valve — normally located between the right ventricle and the pulmonary artery — doesn’t form properly.
Single Ventricle Defects
A single ventricle defect occurs when one of the two pumping chambers in the heart, called ventricles, isn’t large enough or strong enough to work correctly.
Single Ventricle Surgery
The goal of single ventricle surgeries is to enable one ventricle to do the work normally done by two ventricles.
In tricuspid atresia, the tricuspid valve — which is normally located between the right atrium and the right ventricle — is missing, as is the right ventricle.