Midaortic Syndrome

What is midaortic syndrome?

Midaortic syndrome is a very rare condition in which part of the aorta (the heart’s largest blood vessel) that runs through the chest and abdomen becomes narrow. This can lead to lower blood flow in the chest, abdomen and lower limbs.

Midaortic syndrome is also sometimes called narrowing or coarctation of the abdominal aorta. A related condition called renovascular hypertension is high blood pressure that results from decreased blood flow to the kidneys. Both of these conditions are potentially life threatening and require expert care.

Watch this video of Heung Bae Kim, MD, co-director of the Midaortic Syndrome and Renovascular Hypertension Center at Boston Children's Hospital, explaining midaortic syndrome in more detail.


What are the symptoms of midaortic syndrome?

Most children with midaortic syndrome also have renovascular hypertension and have very high blood pressure that can be very difficult to control. Other symptoms of midaortic syndrome vary depending on the individual child but can include:

  • headaches
  • seizures
  • vision changes
  • abdominal pain that begins after a meal
  • discomfort or weakness in the legs after exercise
  • failure to grow properly

Some children with midaortic syndrome have related conditions, such as:

How we care for midaortic syndrome

Midaortic syndrome is a serious condition that requires urgent and thoughtful attention and care. The Midaortic Syndrome and Renovascular Hypertension Center at Boston Children’s Hospital is largest and most experienced multidisciplinary program dedicated to diagnosing and treating children with these conditions. Our team of specialists draws on expertise from nephrology, interventional radiology, cardiology, and vascular surgery to care for children with midaortic syndrome.

Our skilled clinicians offer highly precise diagnostic tests and innovative treatments for midaortic syndrome, including minimally invasive endovascular techniques such as angioplasty and stenting. Some patients may be eligible for Mesenteric Artery Growth Improves Circulation (MAGIC) or Tissue Expander Stimulated Lengthening of the Arteries (TESLA), two pioneering approaches that were developed here at Boston Children’s.