Adamantinoma | Diagnosis & Treatments

How is an adamantinoma diagnosed?

The first step in treating your child is forming an accurate and complete diagnosis. Doctors may use specific tests and procedures to determine the exact type of tumor your child has and whether the tumor has spread. These may include:

  • physical exam, including checking the limb where the tumor is located
  • x-rays, which produce images of internal tissues, bones, and organs onto film
  • magnetic resonance imaging (MRI) to produce detailed images of the area where the tumor is located
  • computerized tomography scan (also called a CT or CAT scan) to capture a detailed view of the body, in some cases
  • biopsy or tissue sample from the tumor to provide definitive information about the type of tumor; this is collected during an image-guided needle biopsy
  • blood and urine tests
  • bone scan to detect bone involvement

After we complete all necessary tests, our experts will meet to review and discuss what they have learned about your child's condition. Then we will meet with you and your family to discuss the results and outline the best treatment options for your child.

What are the treatment options for adamantinoma?

Treatment can vary greatly, depending on your child's situation, including the location and size of the tumor and whether the disease has recurred. Your child's doctor and other members of your care team will discuss the options with you in-depth.

Because adamantinomas do not generally respond to chemotherapy and radiation, the best treatment for your child probably involves surgery. The type of surgery your child receives will depend on the size and location of the tumor, and whether the cancer has spread. Depending on these factors, your child may either need: 

  • limb-salvage surgery to help preserve the limb by removing the tumor and some healthy tissue around the tumor
  • amputation if the tumor cannot be removed by limb-salvage surgery (for example, if the cancer involves major nerves and blood vessels) 

What is the recommended long-term care for children treated for an adamantinoma?

Children treated for an adamantinoma require regular follow-up to screen for recurrence and complications of treatment. A typical follow-up visit may include some or all of the following: 

  • physical exam
  • laboratory testing
  • imaging scans

At these visits, your care team will check on your child's overall health and look for signs that the cancer may have returned.

An adamantinoma that has returned is generally treated through additional surgery.