Pulmonary Vein Stenosis Program

Pulmonary Vein Stenosis Program Overview

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Pulmonary vein stenosis is a rare and serious condition in which there is an obstruction (blockage) in the blood vessels that bring oxygen-rich blood from the lungs back to the heart. It can be isolated to a single pulmonary vein, but most often occurs in multiple veins simultaneously.

The stenosis occurs due to an abnormal thickening and, thus, narrowing of the walls of the veins. Pulmonary vein stenosis frequently progresses. As a result, partial loss or even total obstruction of flow to a vessel or vessels may occur.

Surgery to widen the narrowed veins and catheterization to stretch the vessel are usually short-term solutions since the obstruction typically recurs within a month to six weeks.

Our expertise

The Pulmonary Vein Stenosis team at Boston Children’s coordinates all aspects of care for children with the condition. Because pulmonary vein stenosis is so rare, it’s important that you see a team of specialists who exclusively focus on treating children with this complex condition.

We offer treatment for newly diagnosed patients as well as innovative therapies for children with relapsed pulmonary vein stenosis.

Our specialists are known for treating children with the most complex cases as well as for our expertise in delivering specialized treatments. We often integrate care from other cardiac and pediatric specialties at Boston Children’s Hospital into your child’s treatment plan.

  • Your child’s care team will be led by a pediatric cardiologist and pediatric cardiac nurse practitioner who specialize in treating children with pulmonary vein stenosis.

  • Our team is constantly looking at new and better ways to treat pulmonary vein stenosis, including the innovative use of chemotherapy drugs.

  • Our team works directly with our cardiac surgeons and cardiac catheterization specialists when surgery or balloon dilation (to open the narrowed blood vessel) and/or stenting (using wire tube to prop open the vein) is necessary.

Leaders in the care of children with PVS

At Boston Children's Hospital, we’re fortunate to have a team of cardiac specialists who have been caring for children with pulmonary vein stenosis and have been studying the disease for decades.

Your child’s care team will include:

  • pediatric cardiologists
  • pediatric oncologists
  • cardiac surgeons
  • cardiac catheterization specialists
  • pediatric radiologists
  • pediatric pulmonologists
  • cardiac nurse practitioners
  • research team

At Boston Children's Hospital, we consider you and your child to be integral parts of the care team and not simply recipients of care. You and your team will work together to customize a plan of care for your child.

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This department is currently not accepting appointment requests online. Please call us at: 617-355-6000. International +1-617-355-6000.

This department is currently not accepting appointment requests online. Please call us at: 617-355-6000. International +1-617-355-6000.

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The future of pediatrics will be forged by thinking differently, breaking paradigms and joining together in a shared vision of tackling the toughest challenges before us.”
- Sandra L. Fenwick, President and CEO