Peripheral Pulmonary Stenosis

What is peripheral pulmonary stenosis?

Peripheral pulmonary stenosis is a narrowing in one or more of the branches of the pulmonary arteries. These are the arteries that carry blood from the heart to the lungs.

Peripheral pulmonary stenosis is typically a congenital heart defect — a condition a child is born with. Sometimes peripheral pulmonary stenosis is a complication of a heart defect or genetic syndrome.

Peripheral pulmonary stenosis can cause a lack of oxygen the blood. This can put increased pressure on the heart, making the heart work harder. In some cases, peripheral pulmonary stenosis may get worse over time.

What are the symptoms of peripheral pulmonary stenosis?

Many children in the mild to moderate stages of peripheral pulmonary stenosis have no visible symptoms. Usually, the only symptom is a heart murmur.

As peripheral pulmonary stenosis progresses over time, children may have one or more of the following symptoms:

  • fatigue
  • shortness of breath
  • heavy, difficult breathing
  • rapid, shallow breathing
  • rapid or fluttering heartbeat
  • swelling in the feet, ankles, face or abdomen

What are the causes of peripheral pulmonary stenosis?

Pulmonary stenosis can occur as a complication of other heart conditions, such as tetralogy of Fallot, or in conjunction with certain genetic syndromes that affect the heart, like Williams syndromeAlagille syndrome and Noonan syndrome.

How we care for peripheral pulmonary stenosis

The Boston Children's Hospital Benderson Family Heart Center team has extensive experience treating children, adolescents, and adults with peripheral pulmonary stenosis.

Our specialized training in pediatric cardiology means that we understand the particular challenges, circumstances, and intricacies of working with young people with heart problems.