Midaortic Syndrome | Diagnosis and Treatment

How is midaortic syndrome diagnosed?

Clinicians use a number of tests to diagnose midaortic syndrome. In addition to measuring your child’s blood pressure, our doctors may recommend:

What are the treatment options for midaortic syndrome?

The best treatment approach for midaortic syndrome depends on your child’s unique case. Our physicians will consider a number of factors in weighing treatment options, including:

  • your child’s age and overall health
  • specific symptoms
  • which blood vessels are affected and how extensively
  • whether your child also has renovascular hypertension

We may recommend one or more of the following treatments for your child:

  • Medication to control blood pressure and improve the function of the heart, kidneys or both
  • Minimally invasive endovascular treatments that offer faster recovery times, such as angioplasty or stenting (the placement of a special tube called a stent in a narrowed artery to hold it open).

Depending on the severity of your child’s condition, we may recommend surgical procedures such as:

  • Bypass graft surgery: An operation that makes detours that go around narrowed arteries to create new paths for blood flow
  • Autotransplantation: A procedure which moves one or both kidneys to a new location to improve blood flow
  • Kidney transplant: Transplant is performed when both kidneys are damaged to the point of causing irreversible kidney failure
  • Mesenteric artery growth to improve circulation (MAGIC): MAGIC is a type of innovative surgery that bypasses the aorta using the mesenteric arteries (the arteries that supply blood to the intestines) rather than prosthetic graft material. This can help prevent the need for future graft replacement procedures because the child’s arteries will naturally grow as they get older. This approach was pioneered by surgeons at Boston Children’s and is not offered anywhere else in the world.
  • Tissue Expander Stimulated Lengthening of Arteries (TESLA): TESLA is a novel way of "stretching" the healthy section of the aorta to make it long enough to replace the narrowed part. TESLA was developed by surgeons at Boston Children’s and, while still a new procedure, has had encouraging results in several children with midaortic syndrome.