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Esophageal atresia (EA) is a rare birth defect in which a baby is born without part of the esophagus (the tube that connects the mouth to the stomach). About 1 in 4,000 babies in the U.S. is born with esophageal atresia.
EA frequently occurs along with tracheoesophageal fistula (TEF), and as many as half of all babies with EA/TEF have another birth defect, as well.
The Esophageal Airway Treatment Center at Boston Children's Hospital is one of the only programs in the country specifically designed to care for children with this condition.
Esophageal atresia (EA) is a birth defect in which part of your child’s esophagus is missing. Instead of forming a tube between the mouth and the stomach, the esophagus grows in two separate segments that do not connect.
Esophageal atresia is a lethal disease unless treated. Without a working esophagus, your baby cannot swallow or feed normally. Once esophageal atresia is diagnosed, your child will probably be fed intravenously at the hospital until doctors perform surgery to repair the esophagus.
Although EA can be life-threatening in its most severe forms and could cause long-term nutritional concerns, the majority of children fully recover if it’s detected early.
The best treatment is usually surgery to reconnect the two ends of the baby’s esophagus to each other. In some children, however, so much of the esophagus is missing that the ends can’t be easily connected. This is known as long-gap esophageal atresia.
EA and TEF commonly occur together. In children who have both EA and TEF, the X-ray will show gas in the baby’s stomach (because the esophagus has not formed properly, the only way gas can get into the stomach is through an abnormal channel between the esophagus and the trachea).
After the tests are complete, our team of experts will meet to review and discuss what they have learned about your child's condition. Then we will meet with you and your family to discuss the results and outline the best treatment options.
The exact cause of esophageal atresia is still unknown, but it appears to have some genetic components. Up to half of all babies born with esophageal atresia have one or more other birth defects, such as other digestive tract problems, kidney and urinary tract problems, heart problems or muscular or skeletal problems.
If caught early and treated properly, most babies with esophageal atresia can eat normally within two to three months. Your child may need monitoring for strictures (places of narrowing) in their esophagus, but these are treatable, and in general the outlook is quite good. In fact, the Foker process most often results in an esophagus that looks just like one that developed normally.
After your child is diagnosed with EA, you may feel overwhelmed with information. Your neonatologist or pediatric surgeon may suggest that your child be treated at the hospital where you delivered.
However, given the rarity of this condition and the importance of a successful first treatment (repeated procedures can result in complications), it is important to know all of your options. You want the best possible care for your child, which means working with surgeons who have significant experience treating this condition.
Here are some questions you may want to ask your doctor:
To make an appointment or speak with a member of our team, please call 617-355-3038.
For families residing outside of the United States, please call Boston Children's International Health Services at +01-617-355-5209.
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