Double Outlet Right Ventricle (DORV)

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What is double outlet right ventricle?

Double outlet right ventricle (DORV) is a rare congenital heart defect, meaning it’s a condition a baby is born with. In DORV, the pulmonary artery and the aorta — the heart’s two major arteries — both connect to the right ventricle. In a normal heart, the pulmonary artery connects to the right ventricle, and the aorta connects to the left ventricle. DORV creates a problem because the right ventricle carries oxygen-poor blood, which then gets circulated in the body.

Another heart condition, called a ventricular septal defect (VSD), always occurs with DORV. This is a hole in the tissue wall (septum) that normally separates the right and left ventricles. The VSD allows oxygen-rich blood to pass from the left ventricle to the aorta and pulmonary artery. But even with this added oxygen, the body may still not get enough, causing the heart to work harder.

Normal heart and DORV heart

A child with DORV may also have other heart problems, including:

If your child has DORV, the severity of the condition and type of treatment, including the type of surgical repair, will vary depending on which types of defects he or she has. Although DORV is a serious condition, it is treatable with surgery.

Care for double outlet right ventricle

The experienced surgeons in the Boston Children’s Hospital Cardiac Surgery Department treat some of the most complex pediatric heart conditions in the world, with overall success rates approaching 98 percent — among the highest in the nation among large pediatric cardiac centers. The success rates of the operations used to repair most forms of DORV are in the same range.

At Boston Children’s, we provide families with a wealth of information, resources, programs and support — before, during and after your child’s treatment. With our compassionate, family-centered approach to expert treatment and care, you and your child are in the best possible hands.

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We are grateful to have been ranked #1 on U.S. News & World Report's list of the best children's hospitals in the nation for the third year in a row, an honor we could not have achieved without the patients and families who inspire us to do our very best for them. Thanks to you, Boston Children's is a place where we can write the greatest children's stories ever told.”
- Sandra L. Fenwick, President and CEO

Boston Children's Hospital
300 Longwood Avenue, Boston, MA 02115
For Patients: 617-355-6000 | 800-355-7944

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