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There are many ways you can help children and their families get the care they need.
What treatments are available for cystic lung disease?
Since a cyst may compress your child's airway, it is important that it be removed in a careful and controlled manner. Depending on your child's age, symptoms, and the location of the cyst, it may be possible to remove it via thoracoscopic (minimally invasive) surgery.
To help your child during surgery, the surgeon may include careful ventilation or even use extracorporeal membrane oxygenation (ECMO). This is a machine that takes over for the lungs, providing oxygen and respiratory support.
Even if your child isn't experiencing symptoms from the bronchogenic cyst, it should be removed to prevent long-term complications, including infection, bleeding or malignant degeneration.
There are several ways to treat symptomatic CCAMs. These include:
For lesions that seem to be regressing and are not producing further symptoms, your child's doctors will perform simple post-natal follow up, which will include careful chest imaging and potential delayed pulmonary resection.
Though this course of action is open to debate, some people choose to have these asymptomatic CCAMs removed because of the rare but reported cases of malignant degeneration in these lesions as the babies grow into adults.
A CCAM may also produce neonatal respiratory distress complicated by pulmonary hypertension, and such babies may require urgent neonatal operation and/or aggressive management of their acute respiratory failure including the use of extracorporeal membrane oxygenation (ECMO), a machine that takes over for the lungs, providing oxygen and respiratory support.
Lobar emphysema and pulmonary sequestration
For these conditions, surgery is almost always required to remove the affected lobe (called a lobectomy) in order to prevent further damage to the entire lung. If done promptly, surgical treatment is almost always successful, leaving little or no permanent impairment of breathing capability.
What is the long-term outlook for a child with a cystic lung disease?
Fortunately, children typically do well after the treatment of their cystic lung disease. If they have severe associated anomalies or if the normal lung development has been compromised, then the outcomes may be more limited.
We are grateful to have been ranked #1 on U.S. News & World Report's list of the best children's hospitals in the nation for the third year in a row, an honor we could not have achieved without the patients and families who inspire us to do our very best for them. Thanks to you, Boston Children's is a place where we can write the greatest children's stories ever told.”