Atypical Teratoid Rhabdoid Tumor (ATRT)

An atypical teratoid rhabdoid tumor (AT/RT) is a very rare, aggressive tumor of the central nervous system, occurring mostly in the cerebellum (the part of the brain that controls movement and balance) or the brain stem (the part of the brain that controls basic body functions).

  • AT/RTs usually occur by age 3, but sometimes are found in older children. AT/RTs represent only 1 to 2 percent of childhood brain tumors.
  • These tumors are part of a larger group of malignant tumors called rhabdoid tumors, which also can occur outside the brain.
  • AT/RTs may be localized to one part of the brain, or they can spread to other locations in the brain, spine or body.

How Dana-Farber/Boston Children's Approaches AT/RT Treatment

Children with AT/RTs are treated at Dana-Farber/Boston Children's through our Brain Tumor Center, a world leader in treating this rare disease. Our brain tumor specialists have extensive expertise in treating all types of neural tumors, including AT/RT.

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