Treatments for Anorectal Malformation in Children

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How are anorectal malformations treated?

The majority of babies with anorectal malformation will need to have surgery to correct the problem. The type and number of operations necessary depends on the type and extent of abnormality your baby has.

  • Narrow anal passage

Babies who have the type of malformation that causes the anal passage to be narrow may not need an operation. A procedure known as anal dilatation may be done periodically to help stretch the anal muscles so stool can pass through it easily. However, if the anal opening is positioned wrongly, an operation may be needed to correctly relocate the anal opening.

  • Anal membrane

Babies with this type of malformation will have the membrane removed during surgery. Anal dilatations may need to be done afterward to help prevent any narrowing of the anal passage that is present.

  • Lack of rectal/anal connection (with or without a fistula)

These babies may need a series of operations in order to have the malformation repaired.

Step one: Create a colostomy

With a colostomy, the large intestine is divided into two sections and the ends of intestine are brought through openings in the abdomen. The upper section allows stool to pass through the opening (called a stoma) and then into in a collection bag. The lower section allows mucus that is produced by the intestine to pass into a collection bag.

  • By doing a colostomy, the baby's digestion will not be impaired and she can grow before the time for the next operation.
  • Also, when the next operation is done on the lower section of intestine, there will not be any stool present to infect the area.

The nursing staff and other health care professionals that work with your baby's surgeon can help you learn to take care of the colostomy. Local and national support groups may also be of help to you during this time.

Step two: Attach the rectum to the anus

The next operation attaches the rectum to the anus and is usually done within the first few months of a baby's life. The colostomy remains in place for a few months after this operation so the area can heal without being infected by stool. (Even though the rectum and anus are now connected, stool will leave the body through the colostomy until it is are closed with surgery.) A few weeks after surgery, parents may be performing anal dilatations to help the baby get ready for the next phase of treatment.

Step three: Close the colostomy

Two to three months later, an operation is done to close the colostomy. The baby is not allowed to eat anything for a few days after surgery while the intestine is healing. Several days after surgery, the baby will start passing stools through the rectum.

At first, stools will be frequent and loose. Diaper rash and skin irritation can be a problem at this time. Within a few weeks after surgery, the stools become less frequent and more solid, often causing constipation. Your baby's physician may recommend a high fiber diet (including fruits, vegetables, juices, whole-wheat grains and cereals) to help with constipation.

What's my child's long-term outlook?

Again, it depends on the type of malformation.

  • Children who had the type of malformation that involves an anal membrane or a narrow anal passage are usually able to gain good control over their bowel movements after repair of the anorectal malformation.
  • Children with more complex variations of anorectal malformation may need to participate in a bowel management program in order to help them achieve control over their bowel movements and prevent constipation. The nurses and other health care professionals that work with your child's physicians can help tailor a program to suit your child's needs.

Toilet training should be started at the usual age, which is generally when the child is between two and three years old. However, children who have had anorectal malformations repaired may be slower than others to gain bowel control. Some children may not be able to gain good control over their bowel movements, while others may be chronically constipated, depending on the type of malformation and its repair.

Sometimes these children have difficulty controlling urine and do not properly toilet train, remain wet after training or develop repeated urinary infection. Imaging of the urinary tract with a renal ultrasound and a voiding cystourethrogram (a special bladder x-ray) may help clarify what problem is causing these difficulties.

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