Expansion thoracostomy and insertion of one or more VEPTR" devices is used for the treatment of Thoracic Insufficiency Syndrome.
The goal of this operation is to make one (or both) sides of the chest larger, longer or more normal in shape. A larger chest can provide more room for the lungs to expand or grow. A larger, longer or straighter chest can also help some abnormal spines stay as straight as possible while still allowing for spine growth.
In the expansion thoracostomy operation, one or more separations are made between the ribs and spread apart to make the chest larger. In some expansion thoracostomies, congenitally abnormal, or fused ribs are separated, while in others multiple cuts are made in the ribs or the naturally occurring space between ribs is opened.
During the same operation and after the expansion thoracostomy has taken place, the VEPTR device is attached to the healthy ribs above and below (called a conventional device), or ribs above and spine below (called a hybrid device). Often more than one device is used. For patients with congenitally small chests on both right and left, operations can be done on both sides, but are separated by a long recovery period.
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