Congenital Heart Valve Program Pulmonary valve

LIke ThisLIke ThisLIke ThisLIke ThisLIke This

 

We treat many types of conditions associated with pulmonary valve disease in infants and children. Pulmonary valve disease in the newborn often appears as pulmonary stenosis or a narrowing of the right ventricle. This condition can be treated by our cardiologists in the catheterization lab.  If not treated, the right ventricle may not work properly.

Surgical replacement of the pulmonary valve

The most common surgery performed in adults with congenital heart disease is PVR.  Although new approaches for less invasive replacement of the pulmonary valve are currently being explored, the standard method is surgical placement of a bioprosthetic valve.  Our large experience in PVR has led to a better understanding of the longer-term outcomes after PVR.

Transcatheter pulmonary valve replacement

Since 2007, we have performed 167 transcatheter PVRs.  These procedures are generally performed in our cardiac catheterization lab. Following the procedure, patients are monitored in a short overnight stay and then discharged. Early results have been excellent.

 

Fetal, neonatal and infant pulmonary atresia, pulmonary stenosis and Tetralogy of Fallot

At the Congenital Heart Valve Center, we focus on minimizing the number of operations children need over a lifetime. For example, we often use catheter-based techniques to treat pulmonary valve atresia and/or stenosis during the fetal or neonatal period. However, there are circumstances in which early surgery is necessary.

For example, TOF occurs in many babies born with congenital heart disease. In these cases, we make every effort to rehabilitate the pulmonary valve. With this in mind, many of our patients can be treated with intraoperative balloon dilation of the pulmonary valve. This approach is intended to alleviate or minimize the need for future pulmonary valve replacements.


Advanced imaging for patients with pulmonary valve disease

Many patients with pulmonary valve disease benefit from advanced imaging developed at Boston Children's Hospital. These technologies provide useful information to help determine the ideal timing for a procedure. For example, MRI can help determined the best time to replace the pulmonary valve.

Pulmonary valve clinical studies and trials

We are currently participating in research and clinical trials seeking to minimize the number of operations children and young adults with disease involving the pulmonary valve (such as Tetralogy of Fallot) need over a lifetime. Many of these patients may also benefit from imaging techniques developed at Boston Children's that provide useful information on the right timing for pulmonary valve procedures.

Pulmonary Valve replacement (PVR)

Patients with TOF often develop severe pulmonary regurgitation. In this case, blood flows backward through the valve, causing an enlarged or “dilated” right ventricle. For these patients, a valve replacement is usually recommended. Over the last few years, we have been working with companies to create a pulmonary valve that can be placed without surgery in the catheter lab.

In 2011, the Food and Drug Administration (FDA) approved the use of a new valve for a certain group of patients. The Medtronic Melody Transcatheter Pulmonary Valve is a prosthetic or artificial device that is implanted through a catheter procedure, rather than a more invasive open-heart surgical procedure. This non-surgical approach makes the child's recovery much easier. Cardiologists at Boston Children’s were among the first to use this valve.

Due to wear and tear, the Melody Valve is likely to need replacement over the course of a patient's life. However, because the Melody Valve can be implanted through a catheter, there is minimal risk to the patient.

Timing for Pulmonary Valve replacement

Repairing the pulmonary valve is not possible for all patients. Many times, a pulmonary valve replacement is needed. Over the last decade, cardiologists at Boston Children's have made a strong effort to identify the optimal time for replacement of the pulmonary valve.

Conditions associated with pulmonary valve disease

Tetralogy of Fallot (TOF)

Right ventricle to pulmonary artery conduits

  • Truncus arteriosis
  • Aortic valve disease and Ross procedure

Pulmonary atresaia with intact ventricular septum (PA/IVS)

Endocarditis involving pulmonary valve 

Back to top

Request an Appointment

If this is a medical emergency, please dial 9-1-1. This form should not be used in an emergency.

Patient Information
Date of Birth:
Contact Information
Appointment Details
Send RequestIf you do not see the specialty you are looking for, please call us at: 617-355-6000.International visitors should call International Health Services at +1-617-355-5209.
Please complete all required fields

This department is currently not accepting appointment requests online. Please call us at: 617-355-6000. International +1-617-355-6000.

This department is currently not accepting appointment requests online. Please call us at: 617-355-6000. International +1-617-355-6000.

Thank you.

Your request has been successfully submitted

You will be contacted within 1 business day.

If you have questions or would like more information, please call:

617-355-6000 +1-617-355-6000
close
Find a Doctor
Search by Clinician's Last Name or Specialty:
Select by Location:
Search by First Letter of Clinician's Last Name: *ABCDEFGHIJKLMNOPQRSTUVWXYZ
BrowseSearch
Condition & Treatments
Search for a Condition or Treatment:
Show Items Starting With: *ABCDEFGHIJKLMNOPQRSTUVWXYZ
View allSearch
Locations

Visit the Heart Center Facebook community today!

  • Heart Center at Boston Children's Hospital

    Thank you, CHOB!!! Gabe is 10. Born with a form of HLHS and DS. In 2003 very few children with this dual dx survived for more than a few years. Dr. Del nido found a way. There are no words to express our gratitude. Never give up hope. Pray for direction.Read More

  • Heart Center at Boston Children's Hospital

    Our son Hayden was born 5/12/14 with undiagnosed Transposition of The Great Arteries. He was transferred to Boston Children's and his team of doctors saved his life. He was very sick leading up to his Arterial Switch and... Read More

  • Heart Center at Boston Children's Hospital

    One year ago our little Jonah went in for open heart surgery. He is now 15 months old and is a happy, healthy little boy. We can't thank Dr. Emani and the rest of the crew from the Heart Center at Boston Children's Hospital enough! Little Jonah thanks you too!Read More

  • Heart Center at Boston Children's Hospital

    Michael has two birthday's every year now; born on April 14, and re-born on June 3, 2011. It's been three years now since his heart surgery at Boston Children's Hospital. Michael is doing incredibly well, even ...Read More

  • Heart Center at Boston Children's Hospital

    You would never know our little heart warrior Reece was just at BCH undergoing his 8th heart cath. Thank you to all the doctors, especially Drs. Lock and Marshall, for making sure our little miracle is always smiling!Read More

Support Boston Children's Heart Center

Contact the Congenital Heart Valve Program

The future of pediatrics will be forged by thinking differently, breaking paradigms and joining together in a shared vision of tackling the toughest challenges before us.”
- Sandra L. Fenwick, President and CEO
Close